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Isabella Lawrence

Postdoctoral Associate
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Education

PhD
Newcastle University, Biosciences Institute


BSc
Newcastle University, Biomedical Sciences


About

Titles

Postdoctoral Associate

Appointments

Other Departments & Organizations

Education & Training

PhD
Newcastle University, Biosciences Institute
BSc
Newcastle University, Biomedical Sciences

Research

Publications

2023

2021

  • Bi-allelic variants in the mitochondrial RNase P subunit PRORP cause mitochondrial tRNA processing defects and pleiotropic multisystem presentations.
    Hochberg I, Demain LAM, Richer J, Thompson K, Urquhart JE, Rea A, Pagarkar W, Rodríguez-Palmero A, Schlüter A, Verdura E, Pujol A, Quijada-Fraile P, Amberger A, Deutschmann AJ, Demetz S, Gillespie M, Belyantseva IA, McMillan HJ, Barzik M, Beaman GM, Motha R, Ng KY, O'Sullivan J, Williams SG, Bhaskar SS, Lawrence IR, Jenkinson EM, Zambonin JL, Blumenfeld Z, Yalonetsky S, Oerum S, Rossmanith W, Genomics England Research Consortium, Yue WW, Zschocke J, Munro KJ, Battersby BJ, Friedman TB, Taylor RW, O'Keefe RT, Newman WG. Bi-allelic variants in the mitochondrial RNase P subunit PRORP cause mitochondrial tRNA processing defects and pleiotropic multisystem presentations. Am J Hum Genet 2021, 108: 2195-2204. PMID: 34715011, DOI: 10.1016/j.ajhg.2021.10.002.
    Peer-Reviewed Original Research

Academic Achievements & Community Involvement

Activities

  • activity

    The effect of cellular signalling and nutrient availability on pre-rRNA processing in human cells

  • activity

    The effect of cellular signalling and nutrient availability on pre-rRNA processing in human cells

  • activity

    Drosophila melanogaster as a model to study the ribosomopathy ANE syndrome

Teaching & Mentoring

Mentoring

  • Oteng-Agyei Kankam

    Undergraduate Student
    2024 - Present

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