2024
Cardiac manifestations and outcomes of COVID-19 vaccine-associated myocarditis in the young in the USA: longitudinal results from the Myocarditis After COVID Vaccination (MACiV) multicenter study
Jain S, Anderson S, Steele J, Wilson H, Muniz J, Soslow J, Beroukhim R, Maksymiuk V, Jacquemyn X, Frosch O, Fonseca B, Harahsheh A, Buddhe S, Ashwath R, Thacker D, Maskatia S, Misra N, Su J, Siddiqui S, Vaiyani D, Vaikom-House A, Campbell M, Klein J, Huang S, Mathis C, Cornicelli M, Sharma M, Nagaraju L, Ang J, Uppu S, Ramachandran P, Patel J, Han F, Mandell J, Akam-Venkata J, DiLorenzo M, Brumund M, Bhatla P, Eshtehardi P, Mehta K, Glover K, Dove M, Aldawsari K, Kumar A, Barfuss S, Dorfman A, Minocha P, Yonts A, Schauer J, Cheng A, Robinson J, Powell Z, Srivastava S, Chelliah A, Sanil Y, Hernandez L, Gaur L, Antonchak M, Johnston M, Reich J, Nair N, Drugge E, Grosse-Wortmann L. Cardiac manifestations and outcomes of COVID-19 vaccine-associated myocarditis in the young in the USA: longitudinal results from the Myocarditis After COVID Vaccination (MACiV) multicenter study. EClinicalMedicine 2024, 76: 102809. PMID: 39290640, PMCID: PMC11406334, DOI: 10.1016/j.eclinm.2024.102809.Peer-Reviewed Original ResearchCOVID-19 vaccine-associated myocarditisLate gadolinium enhancementMid-term clinical outcomesVaccine-associated myocarditisCardiac magnetic resonanceMyocardial injuryMulticenter studyClinical diagnosis of acute myocarditisThird dose of mRNA vaccineDiagnosis of acute myocarditisDose of mRNA vaccinePresence of myocardial injuryNo cardiac deathsMedian Follow-UpCohort multicenter studyMultisystem inflammatory syndromeFollow-up informationCardiac manifestationsAcute myocarditisClinical courseInflammatory syndromeClinical presentationGadolinium enhancementCardiac dysfunctionThird doseCardiac phenotype in adolescents and young adults with long-chain 3-hydroxyacyl CoA dehydrogenase (LCHAD) deficiency
Elizondo G, Saini A, Gonzalez de Alba C, Gregor A, Harding C, Gillingham M, Vinocur J. Cardiac phenotype in adolescents and young adults with long-chain 3-hydroxyacyl CoA dehydrogenase (LCHAD) deficiency. Genetics In Medicine 2024, 26: 101123. PMID: 38501492, DOI: 10.1016/j.gim.2024.101123.Peer-Reviewed Original ResearchLong-chain 3-hydroxyacyl-CoA dehydrogenase deficiencyLong-chain 3-hydroxyacyl-CoA dehydrogenaseCardiac involvementCardiac arrestMetabolic decompensationCardiac phenotypeDilated CardiomyopathyLong-chain 3-hydroxyacyl-CoA dehydrogenase deficient patientsEpisodes of metabolic decompensationEnd-stage dilated cardiomyopathyOut-of-hospital cardiac arrestAcute cardiac decompensationIn-hospital cardiac arrestFatty acid oxidation disordersLife-threatening arrhythmiasInfantile dilated cardiomyopathySudden cardiac arrestPotential risk factorsCardiac manifestationsCardiac decompensationRestrictive cardiomyopathyRecurrent episodesRetrospective cohortRisk stratificationPeripheral neuropathy
2023
Beyond Loss of Kidney Function: Patient Care in Autosomal Dominant Polycystic Kidney Disease
Hogan M, Simmons K, Ullman L, Gondal M, Dahl N. Beyond Loss of Kidney Function: Patient Care in Autosomal Dominant Polycystic Kidney Disease. Kidney360 2023, 4: 1806-1815. PMID: 38010035, PMCID: PMC10758524, DOI: 10.34067/kid.0000000000000296.Peer-Reviewed Original ResearchConceptsAutosomal dominant polycystic kidney diseaseDominant polycystic kidney diseasePolycystic kidney diseaseKidney diseaseKidney Disease Improving Global Outcomes guidelinesGlobal Outcomes (KDIGO) guidelinesInitiation of RRTSuccessful kidney transplantEvidence-based guidelinesCurrent clinical practiceKidney stone managementMajor morbidityCardiac manifestationsKidney transplantOutcomes guidelinesKidney functionDepression screeningDisease benefitPancreatic cystsSpecialized careRoutine managementClinical practicePatient careStone managementDisease aspectsCardiac manifestations of multisystem inflammatory syndrome of children after SARS-CoV-2 infection: a systematic review and meta-analysis.
Carmona C, Kuziez M, Freitas C, Cyrus J, Bain J, Karam O. Cardiac manifestations of multisystem inflammatory syndrome of children after SARS-CoV-2 infection: a systematic review and meta-analysis. Cardiology In The Young 2023, 33: 2319-2327. PMID: 36762563, DOI: 10.1017/s104795112300015x.Peer-Reviewed Original ResearchConceptsMultisystem inflammatory syndromeInflammatory syndromeCardiac manifestationsSystematic reviewSARS-CoV-2 infectionCommon cardiac manifestationVentricular systolic dysfunctionSARS-CoV-2 pandemicCoronary abnormalitiesSystolic dysfunctionHospital periodMembrane oxygenationOvid EmbasePatient outcomesOvid MEDLINEChild patientsLarge cohortAccurate prevalenceElectronic searchMortality rateLiterature databasesPrevalenceSyndromeFull textManifestations
2022
Coronavirus disease 2019 and the young heart: prevention, treatment, and return to play
Beach CM, Faherty E, Pesce M. Coronavirus disease 2019 and the young heart: prevention, treatment, and return to play. Current Opinion In Pediatrics 2022, 34: 471-475. PMID: 36036422, PMCID: PMC9593324, DOI: 10.1097/mop.0000000000001167.Peer-Reviewed Reviews, Practice Guidelines, Standards, and Consensus StatementsConceptsCOVID-19 vaccinationRisk factorsSevere diseasePhysical activitySevere acute respiratory syndrome coronavirus 2 (SARS-CoV-2) transmissionAcute COVID-19 infectionAcute COVID-19Regular physical activityViral prevalenceCOVID-19 infectionSpecific risk factorsCoronavirus disease 2019Current care modelsPrevention of diseaseInflammatory syndromeCardiac manifestationsPoor outcomeDisease 2019Care modelYoung heartsViral transmissionInfectionDiseaseCOVID-19VaccinationCardiac crises: Cardiac arrhythmias and cardiomyopathy during TANGO2 deficiency related metabolic crises
Miyake CY, Lay EJ, Beach CM, Ceresnak SR, Delauz CM, Howard TS, Janson CM, Jardine K, Kannankeril PJ, Kava M, Kim JJ, Liberman L, Macicek SL, Pham TD, Robertson T, Valdes SO, Webster G, Stephens SB, Milewicz DM, Azamian M, Ehsan SA, Houck KM, Soler-Alfonso C, Glinton KE, Tosur M, Li N, Xu W, Lalani SR, Zhang L. Cardiac crises: Cardiac arrhythmias and cardiomyopathy during TANGO2 deficiency related metabolic crises. Heart Rhythm 2022, 19: 1673-1681. PMID: 35568137, PMCID: PMC10642301, DOI: 10.1016/j.hrthm.2022.05.009.Peer-Reviewed Original ResearchConceptsVentricular tachycardiaCardiac crisisCardiac arrestMetabolic crisisIntravenous magnesiumAtrial pacingCardiac arrhythmiasRetrospective multicenter chart reviewType I Brugada patternInitiation of feedsMulticenter chart reviewMembrane oxygenation supportCurrent treatment optionsAutosomal recessive diseaseLethal cardiac arrhythmiasBrugada patternOxygenation supportCardiac manifestationsChart reviewQTc prolongationAntiarrhythmic drugsHeart blockSupraventricular tachycardiaTreatment optionsSuccessful treatment
2021
One gene, two modes of inheritance, four diseases: A systematic review of the cardiac manifestation of pathogenic variants in JPH2-encoded junctophilin-2
Parker L, Kramer R, Kaplan S, Landstrom A. One gene, two modes of inheritance, four diseases: A systematic review of the cardiac manifestation of pathogenic variants in JPH2-encoded junctophilin-2. Trends In Cardiovascular Medicine 2021, 33: 1-10. PMID: 34861382, PMCID: PMC9156715, DOI: 10.1016/j.tcm.2021.11.006.Peer-Reviewed Original ResearchConceptsSudden cardiac deathDilated CardiomyopathyHypertrophic cardiomyopathyCardiac diseaseMode of inheritanceEarly onset DCMCardiac conduction diseaseVariant-positive individualsLoss-of-function variantsCorrelated clinical phenotypesDominant missense variantsSystematic reviewCardiac manifestationsConduction diseaseCase reportCardiac deathPathogenic variantsClinical phenotypeMissense variantsJPH2Rare variantsDiseaseCardiomyopathyArrhythmiasVariants
2019
Cardiac Manifestations of Noonan Syndrome.
Karnik R, Geiger M. Cardiac Manifestations of Noonan Syndrome. Pediatric Endocrinology Reviews : PER 2019, 16: 471-476. PMID: 31115199, DOI: 10.17458/per.vol16.2019.kpg.manifestationsnoonan.Peer-Reviewed Reviews, Practice Guidelines, Standards, and Consensus StatementsConceptsLong-term prognosisDevelopment of cardiomyopathyCommon structural abnormalityPulmonary stenosisCardiac manifestationsMedical therapyTerm prognosisCardiovascular abnormalitiesHypertrophic cardiomyopathyCardiac diseaseCardiac pathologyStructural abnormalitiesRAF1 mutationsNoonan syndromePTPN11 mutationsInvolved pathwaysCardiomyopathyGenotype-phenotype associationsAbnormalitiesWide spectrumAssociationStenosisPrognosisSyndromeInfants
2017
Neuromuscular Disease Cardiac Manifestations and Sudden Death Risk
Limipitikul W, Ong CS, Tomaselli GF. Neuromuscular Disease Cardiac Manifestations and Sudden Death Risk. Cardiac Electrophysiology Clinics 2017, 9: 731-747. PMID: 29173414, DOI: 10.1016/j.ccep.2017.07.013.Peer-Reviewed Original ResearchConceptsNeuromuscular diseaseSudden death riskPresence of bradycardiaConduction system diseaseCardiac conduction systemCardiovascular complicationsCardiac manifestationsPreemptive treatmentHeart blockSignificant morbidityVentricular arrhythmiasPermanent pacemakerDeath riskSystem diseasesCardiac arrhythmiasConduction systemDiseasePatientsArrhythmiasRiskBradycardiaMorbidityComplicationsTachyarrhythmiasMortality
2002
Spectrum and progression of conduction abnormalities in infants born to mothers with anti-SSA/Ro-SSB/La antibodies
Askanase A, Friedman D, Copel J, Dische M, Dubin A, Starc T, Katholi M, Buyon J. Spectrum and progression of conduction abnormalities in infants born to mothers with anti-SSA/Ro-SSB/La antibodies. Lupus 2002, 11: 145-151. PMID: 11999879, DOI: 10.1191/0961203302lu173oa.Peer-Reviewed Original ResearchConceptsSSA/Ro-SSB/La antibodiesThird-degree blockCongenital heart blockLa antibodiesSecond-degree blockConduction abnormalitiesDegree blockNeonatal lupusHeart blockAV blockAtrial rateAV nodeAntibody-mediated inflammationMean atrial rateAdvanced AV blockTime of surgeryFirst-degree blockSpectrum of arrhythmiasNormal sinus rhythmAge 10 yearsIncomplete AV blockCardiac manifestationsNodal involvementSinus bradycardiaSubsequent fibrosis
1992
Endovascular Infections Arising from Right-Sided Heart Structures
Remetz M, Quagliarello V. Endovascular Infections Arising from Right-Sided Heart Structures. Cardiology Clinics 1992, 10: 137-149. PMID: 1739955, DOI: 10.1016/s0733-8651(18)30259-5.Peer-Reviewed Original ResearchConceptsRight-sided endocarditisRight-sided heart failureLeft-sided endocarditisAntibiotic therapyHeart failureClinical manifestationsWorse prognosisTricuspid valveEndovascular infectionProgressive right-sided heart failureS. aureusMultiple septic pulmonary emboliSeptic pulmonary emboliInitial antibiotic therapyCombination antibiotic therapyCommon predisposing factorsCases of endocarditisCongenital heart diseaseViridans group streptococciCoexistent infectionPleuritic painProductive coughSignificant murmurPulmonary infarctionCardiac manifestations
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