2020
Multi-dimensional clinical phenotyping of a national cohort of adult cystic fibrosis patients
Conrad D, Billings J, Teneback C, Koff J, Rosenbluth D, Bailey B, Jain R. Multi-dimensional clinical phenotyping of a national cohort of adult cystic fibrosis patients. Journal Of Cystic Fibrosis 2020, 20: 91-96. PMID: 32948498, DOI: 10.1016/j.jcf.2020.08.010.Peer-Reviewed Original ResearchConceptsCystic fibrosis transmembrane conductance regulatorCF patientsCystic fibrosisClinical phenotypeChronic P. aeruginosa infectionDistal intestinal obstruction syndromeAdult cystic fibrosis patientsPseudomonas aeruginosa colonizationUS CF centersAdult CF patientsIntestinal obstruction syndromeTransmembrane conductance regulatorHigh-risk phenotypeWell-nourished groupCholestatic liver diseaseGroup of patientsCystic fibrosis patientsRates of pancreatic insufficiencyMulti-system disorderPancreatic malabsorptionObstruction syndromeChronic sinusitisConductance regulatorPancreatic insufficiencyCF centers32 Meconium Disease
Escobar M, Caty M. 32 Meconium Disease. 2020, 517-535. DOI: 10.1016/b978-0-323-54940-0.00032-8.Peer-Reviewed Original ResearchClinical manifestations of cystic fibrosisMeconium plug syndromeNeonatal intensive care unitDistal intestinal obstruction syndromeCF transmembrane regulatorMeconium ileusManifestations of cystic fibrosisEmergent operative explorationCongenital bilateral absenceIntestinal obstruction syndromeBiliary tract diseaseClearance of secretionsLong-term complicationsGastroesophageal reflux diseaseIntensive care unitAssociated with CFPulmonary managementFibrosing colonopathyComplications of MIContrast enemaMeconium diseaseBilateral absenceNewborn periodObstruction syndromeTransmembrane regulator
2015
Gastrointestinal Disorders in Cystic Fibrosis
Assis DN, Freedman SD. Gastrointestinal Disorders in Cystic Fibrosis. Clinics In Chest Medicine 2015, 37: 109-118. PMID: 26857772, DOI: 10.1016/j.ccm.2015.11.004.BooksConceptsCystic fibrosisDistal intestinal obstruction syndromeCommon GI complicationsIntestinal obstruction syndromeCare of patientsGI complicationsGastrointestinal manifestationsObstruction syndromeGI disordersGI malignanciesIntestinal overgrowthPulmonary functionClinical presentationGastrointestinal disordersPancreatic insufficiencyInnovative therapiesRecent approvalModulating agentsFibrosisDisordersComplicationsPatientsMalignancySyndromeTherapy
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