2018
Gastrointestinal and Extra-Intestinal Manifestations of IgG4–Related Disease
Miyabe K, Zen Y, Cornell LD, Rajagopalan G, Chowdhary VR, Roberts LR, Chari ST. Gastrointestinal and Extra-Intestinal Manifestations of IgG4–Related Disease. Gastroenterology 2018, 155: 990-1003.e1. PMID: 30012334, DOI: 10.1053/j.gastro.2018.06.082.Peer-Reviewed Original ResearchConceptsIgG4-RDPlasma cellsExtra-intestinal manifestationsHuman IgG4-RDSimilar immune reactionsRelapsing-remitting courseDense lymphoplasmacytic infiltrateTiters of autoantibodiesMulti-organ diseasePermanent organ damageObliterative phlebitisStoriform fibrosisAutoimmune etiologyMetachronous lesionsPrimary therapyExcellent prognosisLymph nodesLymphoplasmacytic infiltrateSerum levelsOrgan damageSerum IgG4Bile ductAutoimmune diseasesTypical presentationInflammatory response
2015
IgG4-Sclerosing Cholangitis in a Pediatric Patient
Rosen D, Thung S, Sheflin-Findling S, Lai J, Rosen A, Arnon R, Chu J. IgG4-Sclerosing Cholangitis in a Pediatric Patient. Seminars In Liver Disease 2015, 35: 089-094. PMID: 25632939, DOI: 10.1055/s-0034-1398475.Peer-Reviewed Original ResearchConceptsPrimary sclerosing cholangitisIgG4-SCPediatric patientsSerum IgG4Characteristic pathology findingsBile duct stricturesImmune-mediated processElevated serum IgG4Bile duct wallReversal of diseaseAsymptomatic elevationObliterative phlebitisAbdominal painSclerosing cholangitisDuct stricturesAutoimmune pancreatitisObstructive jaundicePediatric gastroenterologistsPathology findingsExtensive fibrosisLymphoplasmacellular infiltrationLiver enzymesDisease entityAppropriate treatmentPlasma cells
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