2022
An update on ductal plate malformations and fibropolycystic diseases of the liver
Mirza H, Besse W, Somlo S, Weinreb J, Kenney B, Jain D. An update on ductal plate malformations and fibropolycystic diseases of the liver. Human Pathology 2022, 132: 102-113. PMID: 35777701, DOI: 10.1016/j.humpath.2022.06.022.Peer-Reviewed Original ResearchConceptsDuctal plate malformationLiver diseaseAdult polycystic liver diseaseAutosomal dominant polycystic kidneyFibropolycystic liver diseaseIsolated liver involvementCongenital hepatic fibrosisPolycystic liver diseaseVon Meyenburg complexesGenetic underpinningsMultiple clinical phenotypesFibropolycystic diseasePortal hypertensionCaroli's diseaseLiver involvementLiver cystsMeyenburg complexesHepatic fibrosisFibrocystic lesionsHepatocellular malignanciesCyst enlargementAbnormal organ developmentPolycystic kidneysAnimal modelsHepatocellular malignancy
1989
Hepatic fibropolycystic disease in Mexico. Study of 82 cases.
Torres-Barrera G, García-Tsao G, Quiroz F, Ferrari. Hepatic fibropolycystic disease in Mexico. Study of 82 cases. Revista De Investigación Clínica 1989, 41: 45-52. PMID: 2727432.Peer-Reviewed Original ResearchConceptsCongenital hepatic fibrosisFibropolycystic diseaseLiver function testsPolycystic liver diseaseHepatic fibrosisCholedochal cystCaroli's diseaseLiver diseaseFunction testsMean agePolycystic kidneysInstituto Nacional de la NutriciónRenal insufficiencyVariceal hemorrhageSalvador ZubiránPolycystic diseaseIsolated diseaseIndividual patientsLarge seriesFibrosisCholangitisDiseasePatientsCystsKidney
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