Featured Publications
Hair and skin predict cardiomyopathies: Carvajal and erythrokeratodermia cardiomyopathy syndromes
Sun Q, Lee L, Hall EK, Choate KA, Elder RW. Hair and skin predict cardiomyopathies: Carvajal and erythrokeratodermia cardiomyopathy syndromes. Pediatric Dermatology 2020, 38: 31-38. PMID: 33275305, DOI: 10.1111/pde.14478.Peer-Reviewed Original ResearchConceptsCongestive heart failureCardiac evaluationHeart failureHeart diseaseSudden deathNail abnormalitiesCardiac pathologyNovel therapeuticsCardiomyopathy syndromeFatal consequencesYoung childrenPatientsWarning signsSyndromeFamily membersCardiocutaneous disorderSkinCharacteristic hairCardiomyopathyAbnormalitiesDiseasePathology
2019
Modern Day Care of Patients With Single Ventricle Heart Disease: Late Complications of Fontan Palliation
Simmons M, Elder R. Modern Day Care of Patients With Single Ventricle Heart Disease: Late Complications of Fontan Palliation. Current Pediatrics Reports 2019, 7: 53-61. DOI: 10.1007/s40124-019-00192-7.Peer-Reviewed Original ResearchFontan palliationSingle ventricle heart diseaseLate hepatic complicationsHepatic complicationsPulmonary vasodilatorsReviewThe majorityFontan failureVascular complicationsFontan operationLate complicationsHeart failureHeart diseaseLymphatic complicationsNovel therapiesLiver cancerHigh riskComplicationsRecent FindingsRecentScoring systemPatientsDay carePalliationTherapyStructural complicationsSeparate entities
2013
Hemodynamic Phenotype of the Failing Fontan in an Adult Population
Hebson CL, McCabe NM, Elder RW, Mahle WT, McConnell M, Kogon BE, Veledar E, Jokhadar M, Vincent RN, Sahu A, Book WM. Hemodynamic Phenotype of the Failing Fontan in an Adult Population. The American Journal Of Cardiology 2013, 112: 1943-1947. PMID: 24075283, PMCID: PMC4505550, DOI: 10.1016/j.amjcard.2013.08.023.Peer-Reviewed Original ResearchConceptsFontan failureCardiac indexFontan patientsLiver diseaseSVR indexLower systemic vascular resistance indexNormal systolic ventricular functionSystemic vascular resistance indexAdult Fontan patientsSimilar cardiac indexSystolic ventricular functionVascular resistance indexSignificant liver diseasePediatric Fontan patientsCase-cohort analysisFailing FontanPF cohortsPortal hypertensionAdult patientsCatheterization findingsFontan circulationHeart failureVentricular functionCirculatory derangementsPediatric cohort