2023
Liver Transplantation for Mahvash Disease, an Inborn Error of Metabolism
Mistry P, Garcia-Tsao G. Liver Transplantation for Mahvash Disease, an Inborn Error of Metabolism. New England Journal Of Medicine 2023, 389: 2010-2013. PMID: 37991861, DOI: 10.1056/nejme2310332.Peer-Reviewed Original Research
2010
Long-Term Outcomes of Liver Transplantation in Type 1 Gaucher Disease
Ayto RM, Hughes DA, Jeevaratnam P, Rolles K, Burroughs AK, Mistry PK, Mehta AB, Pastores GM. Long-Term Outcomes of Liver Transplantation in Type 1 Gaucher Disease. American Journal Of Transplantation 2010, 10: 1934-1939. PMID: 20659098, DOI: 10.1111/j.1600-6143.2010.03168.x.Peer-Reviewed Original ResearchMeSH KeywordsAdolescentAdultChildEnzyme Replacement TherapyFatal OutcomeFemaleGaucher DiseaseHumansLiver FailureLiver TransplantationMaleTreatment OutcomeConceptsEnzyme replacement therapyLiver transplantationGaucher diseaseLong-term enzyme replacement therapyEnd-stage liver diseaseType 1 Gaucher's diseaseSevere hepatic impairmentOrthotopic liver transplantationSuccessful liver transplantationLife-saving treatmentPrevalent lysosomal storage disorderHepatic impairmentLysosomal storage disorderYears postprocedureLiver failureLiver diseaseTerm outcomesReplacement therapyExcellent outcomesDemonstrable efficacyPatientsTransplantationPathological manifestationsDiseaseStorage disorderLiver transplantation for inherited metabolic disorders of the liver
Moini M, Mistry P, Schilsky ML. Liver transplantation for inherited metabolic disorders of the liver. Current Opinion In Organ Transplantation 2010, 15: 269-276. PMID: 20489626, DOI: 10.1097/mot.0b013e3283399dbd.Peer-Reviewed Original ResearchConceptsLiver transplantExtrahepatic diseaseLiver transplantationGlycogen storage disease type ICareful patient selectionOutcome of transplantationImportant therapeutic modalityMultisystemic genetic disorderMajor hepatic diseasesUrea cycle defectsGene replacement therapyHepatic complicationsSurgical managementLiver replacementMetabolic managementPatient selectionPrimary hyperoxaluriaReplacement therapyHepatic diseaseImproved outcomesTherapeutic modalitiesMetabolic disordersMetabolic diseasesTransplantLiver results
2005
Hepatocellular Carcinoma in Type 1 Gaucher Disease: A Case Report with Review of the Literature
Xu R, Mistry P, Mckenna G, Emre S, Schiano T, Bu-Ghanim M, Levi G, Fiel M. Hepatocellular Carcinoma in Type 1 Gaucher Disease: A Case Report with Review of the Literature. Seminars In Liver Disease 2005, 25: 226-229. PMID: 15918150, DOI: 10.1055/s-2005-871201.Peer-Reviewed Original ResearchMeSH KeywordsCarcinoma, HepatocellularFemaleGaucher DiseaseHumansLiverLiver NeoplasmsLiver TransplantationMiddle AgedConceptsType 1 Gaucher diseaseHepatocellular carcinomaGaucher diseaseLiver transplantationInborn errorsType 1 Gaucher's diseaseNecessitating liver transplantationNon-neuronopathic diseaseDevelopment of cirrhosisMajority of patientsStandard of careRisk of malignancyEnzyme replacement therapyDeficiency of glucocerebrosidaseRare inborn errorVariety of neoplasmsAutosomal recessive disorderMarrow infiltrationPulmonary diseaseSupplemental therapyReplacement therapyCase reportLysosomal storage diseaseTissue macrophagesType 2
2001
Blood and graft eosinophils in acute cellular rejection of liver allografts
Nagral A, Quaglia A, Sabin CA, Dhillon AP, Bearcroft CP, Millar A, Davies SE, Mistry PK, Davidson BR, Rolles K, Burroughs AK. Blood and graft eosinophils in acute cellular rejection of liver allografts. Transplantation Proceedings 2001, 33: 2588-2593. PMID: 11406255, DOI: 10.1016/s0041-1345(01)02105-4.Peer-Reviewed Original Research
1999
MYCOPHENOLATE MOFETIL MONOTHERAPY IN STABLE LIVER TRANSPLANT PATIENTS WITH CYCLOSPORINE-INDUCED RENAL IMPAIRMENT
Papatheodoridis G, O'Beirne J, Mistry P, Davidson B, Rolles K, Burroughs A. MYCOPHENOLATE MOFETIL MONOTHERAPY IN STABLE LIVER TRANSPLANT PATIENTS WITH CYCLOSPORINE-INDUCED RENAL IMPAIRMENT. Transplantation 1999, 68: 155-157. PMID: 10428285, DOI: 10.1097/00007890-199907150-00029.Peer-Reviewed Original ResearchConceptsStable liver transplant patientsLiver transplant patientsMajor side effectsTransplant patientsRenal impairmentMycophenolate mofetilSide effectsMycophenolate mofetil monotherapyReduction of cyclosporineSerum creatinine levelsEfficacy of monotherapyCellular rejectionIntravenous courseMaintenance immunosuppressantsMofetil monotherapyMycophenolate monotherapyCreatinine levelsSubtherapeutic levelsMonotherapyPatientsSignificant riskMonthsImpairmentMofetilCyclosporine
1998
Ulcerative colitis has an aggressive course after orthotopic liver transplantation for primary sclerosing cholangitis
Papatheodoridis GV, Hamilton M, Mistry PK, Davidson B, Rolles K, Burroughs AK. Ulcerative colitis has an aggressive course after orthotopic liver transplantation for primary sclerosing cholangitis. Gut 1998, 43: 639. PMID: 9824344, PMCID: PMC1727300, DOI: 10.1136/gut.43.5.639.Peer-Reviewed Original ResearchConceptsPrimary sclerosing cholangitisInflammatory bowel diseaseLong-term steroidsUlcerative colitisSclerosing cholangitisBowel diseaseLiver transplantationAggressive courseTerm steroidsDe novo ulcerative colitisNew-onset ulcerative colitisInflammatory bowel disease activityBowel disease activityOnset ulcerative colitisOrthotopic liver transplantationEarly colorectal neoplasmsMaintenance immunosuppressionQuiescent courseDisease activityTransplant patientsPrevious colectomyColorectal cancerColorectal neoplasmsColitisPatientsCombined liver-kidney transplantation in methylmalonic acidemia
van 't Hoff WG, Dixon M, Taylor J, Mistry P, Rolles K, Rees L, Leonard JV. Combined liver-kidney transplantation in methylmalonic acidemia. The Journal Of Pediatrics 1998, 132: 1043-1044. PMID: 9627602, DOI: 10.1016/s0022-3476(98)70407-x.Peer-Reviewed Original ResearchOutcome of orthotopic liver transplantation in patients with haemophilia
Gordon FH, Mistry PK, Sabin CA, Lee CA. Outcome of orthotopic liver transplantation in patients with haemophilia. Gut 1998, 42: 744. PMID: 9659174, PMCID: PMC1727096, DOI: 10.1136/gut.42.5.744.Peer-Reviewed Original ResearchConceptsOrthotopic liver transplantationHepatitis C cirrhosisHuman immunodeficiency virusLiver transplantationC cirrhosisViral hepatitisHepatocellular carcinomaHIV-negative recipientsRecurrent viral hepatitisChronic viral hepatitisHIV-positive recipientsKaplan-Meier analysisLong-term outcomesLong-term cureMedical database searchHaemophilic menPositive recipientsHepatitis BBiliary atresiaCommon indicationDisease recurrenceHIV infectionTransplant centersMedian timeNegative recipients