Lessons from lung transplantation: Cause for redefining the pathophysiology of pulmonary hypertension in gaucher disease
Goobie GC, Sirrs SM, Yee J, English JC, Bergeron C, Nador R, Swiston JR, Mistry PK, Paquin W, Levy RD. Lessons from lung transplantation: Cause for redefining the pathophysiology of pulmonary hypertension in gaucher disease. Respiratory Medicine Case Reports 2019, 28: 100893. PMID: 31334026, PMCID: PMC6624456, DOI: 10.1016/j.rmcr.2019.100893.Peer-Reviewed Original ResearchGaucher disease type 1Bilateral sequential lung transplantationPulmonary hypertensionLung transplantationGaucher cellsSuccessful bilateral sequential lung transplantationEnd-stage pulmonary hypertensionGroup 1 pulmonary hypertensionPre-transplant comorbiditiesPulmonary parenchymal diseasePulmonary vasodilator therapyPost-transplant courseSevere pulmonary hypertensionAcute renal failurePulmonary arterial hypertensionExtracorporeal membrane oxygenationInterstitial lung diseaseLong-term treatmentPrevious case reportsEnzyme replacement therapyDisease type 1Vasodilator therapyArterial hypertensionLung transplantPrior splenectomy