A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo.
French PJ, van Doorninck JH, Peters RH, Verbeek E, Ameen NA, Marino CR, de Jonge HR, Bijman J, Scholte BJ. A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo. Journal Of Clinical Investigation 1996, 98: 1304-1312. PMID: 8823295, PMCID: PMC507556, DOI: 10.1172/jci118917.Peer-Reviewed Original Research