Liver transplantation for glycogen storage disease type Ia
Reddy SK, Austin SL, Spencer-Manzon M, Koeberl DD, Clary BM, Desai DM, Smith AD, Kishnani PS. Liver transplantation for glycogen storage disease type Ia. Journal Of Hepatology 2009, 51: 483-490. PMID: 19596478, DOI: 10.1016/j.jhep.2009.05.026.Peer-Reviewed Original ResearchConceptsGSD Ia patientsLiver transplantationIA patientsHepatocellular carcinomaHepatocellular adenomaRenal dysfunctionPrevention of HCCGSD IaMultiple hepatocellular adenomasPost-transplant complicationsPre-operative comorbiditiesGlycogen storage disease typeDefinitive preventionImmunosuppressive medicationsAllograft rejectionCytomegalovirus infectionRenal functionTotal cholesterolHemoglobin levelsMetabolic derangementsSerum triglyceridesRetrospective studyUnited NetworkPrincipal indicationBlood glucose