Ocular Manifestations of Inherited Phospholipase-C&ggr;2–Associated Antibody Deficiency and Immune Dysregulation
Di Zazzo A, Tahvildari M, Florakis G, Dana R. Ocular Manifestations of Inherited Phospholipase-C&ggr;2–Associated Antibody Deficiency and Immune Dysregulation. Cornea 2016, 35: 1656-1657. PMID: 27442322, PMCID: PMC5250612, DOI: 10.1097/ico.0000000000000951.Peer-Reviewed Original ResearchConceptsOcular manifestationsOcular surfaceAntibody deficiencyImmune dysregulationEpisodes of ocular inflammationInterleukin-1Anti-IL-1 therapySystemic immunomodulatory treatmentSystemic side effectsBouts of inflammationInterstitial lung diseaseRecurrent inflammatory diseaseInterleukin-1 productionCorneal pannusCorneal involvementCorneal scarringOcular inflammationOral prednisoneOcular symptomsSystemic immunosuppressionImmunomodulatory treatmentSystemic manifestationsLung diseaseActive lesionsPartial improvement
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