2018
Liver Transplantation for Wilson Disease
Miloh T, Schilsky M. Liver Transplantation for Wilson Disease. Clinical Gastroenterology 2018, 183-202. DOI: 10.1007/978-3-319-91527-2_11.Peer-Reviewed Original ResearchAcute liver failureLiver transplantationLiver failureWilson's diseaseChronic end-stage liver diseaseEnd-stage liver disease (MELD) scoreNon-resectable liver cancerEnd-stage liver diseaseHeterotopic liver transplantationLiver Disease scoreRisk of morbidityStatus 1APortal hypertensionLiver donationLiver diseaseLiver functionCell transplantationLifelong immunosuppressionTransplant surgeryChronic diseasesDonor organsLiver cancerWait listDisease scorePatients
2011
Wilson Disease: Pathogenesis and Clinical Considerations in Diagnosis and Treatment
Rosencrantz R, Schilsky M. Wilson Disease: Pathogenesis and Clinical Considerations in Diagnosis and Treatment. Seminars In Liver Disease 2011, 31: 245-259. PMID: 21901655, DOI: 10.1055/s-0031-1286056.Peer-Reviewed Original ResearchConceptsPathologic findingsWilson's diseaseHepatocyte cell transplantationLife-long treatmentInitiation of treatmentKayser-Fleischer ringsFirst-degree relativesPresence of signsBiliary copper excretionLiver transplantationMedical therapyLow ceruloplasminCell transplantationElevated urineLenticular degenerationHistologic changesDisease progressionClinical signsFatal disorderNeurologic diseaseAnimal modelsClinical considerationsCopper excretionDiseaseEarly detection